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Clinics in Perinatology Jun 1989Care of an infant with myelomeningocele may begin with prenatal diagnosis, which allows for optimal perinatal care. In the newborn period, the decision for surgical... (Review)
Review
Care of an infant with myelomeningocele may begin with prenatal diagnosis, which allows for optimal perinatal care. In the newborn period, the decision for surgical treatment of myelomeningocele must be made promptly, but only after rational discussion with, and consent by, the affected child's family. Advances in newborn care and in surgical techniques, and an improved ability to both detect and treat hydrocephalus and CSF infections, have resulted in better outcomes for these children. Recent insights into the pathogenesis of myelomeningocele suggest that prevention of most of these congenital malformations may be possible through periconceptual vitamin supplementation.
Topics: Humans; Infant, Newborn; Meningomyelocele; Prenatal Diagnosis
PubMed: 2663304
DOI: No ID Found -
The Urologic Clinics of North America Aug 2004Disordered innervation of the detrusor musculature and external sphincter in patients with myelomeningocele adversely affects bladder function and potentially threatens... (Review)
Review
Disordered innervation of the detrusor musculature and external sphincter in patients with myelomeningocele adversely affects bladder function and potentially threatens the upper urinary tracts. Children with this condition can be categorized into high and low- risk groups for secondary damage from a neurogenic bladder based on intravesical pressure. Those with elevated pressure are at risk for hydronephrosis or reflux,and evidence suggests that early management of high pressure protects the bladder from additional damage, reducing the need for augmentation. Management decisions made during infancy potentially impact long-term outcomes for preserving renal function and achieving urinary continence. This discussion focuses on the initial urologic care of infants with myelomeningocele, emphasizing the controversy regarding urodynamic versus radiologic-based management of the neurogenic bladder.
Topics: Humans; Infant, Newborn; Meningomyelocele; Radiography; Urinary Bladder, Neurogenic; Urodynamics
PubMed: 15313052
DOI: 10.1016/j.ucl.2004.04.001 -
Child's Nervous System : ChNS :... Dec 2014
Topics: Female; Humans; Male; Meningomyelocele; Plastic Surgery Procedures; Surgical Flaps
PubMed: 25227168
DOI: 10.1007/s00381-014-2550-0 -
Neurosurgery Clinics of North America Jul 2017Myelomeningocele (MMC) is a costly lifetime disease with many comorbidities, including sensory and motor lower limb disability, bladder/bowel dysfunction, scoliosis,... (Comparative Study)
Comparative Study Review
Myelomeningocele (MMC) is a costly lifetime disease with many comorbidities, including sensory and motor lower limb disability, bladder/bowel dysfunction, scoliosis, club foot, and hydrocephalus. MMC treatment options have changed over time because routine use of fetal ultrasonography and MRI has provided prenatal diagnosis and the potential for fetal surgery. There is still no consensus on how to treat the MMC diagnoses prenatally, mainly related to the infrastructure required to operate on pregnant patients. This article provides an overview of prenatal and postnatal MMC repair and the features in the prenatal diagnosis.
Topics: Comorbidity; Female; Humans; Meningomyelocele; Pregnancy; Prenatal Diagnosis
PubMed: 28600017
DOI: 10.1016/j.nec.2017.02.005 -
Revista Brasileira de Ginecologia E... Nov 2015
Topics: Female; Fetus; Humans; Meningomyelocele; Pregnancy
PubMed: 26561237
DOI: 10.1590/SO100-720320150005473 -
Child's Nervous System : ChNS :... Jul 2017To assess the role of magnetic resonance imaging (MRI) in the management of myelomenigocele. (Review)
Review
OBJECTIVE
To assess the role of magnetic resonance imaging (MRI) in the management of myelomenigocele.
BACKGROUND
Spinal dysraphism or neural tube defects (NTD) encompass a heterogeneous group of congenital spinal anomalies that result from the defective closure of the neural tube early in gestation. Myelomeningocele is the most common type of NTD that is compatible with life, with high survival rates but lifelong physical impairments.
CONCLUSION
MRI is an important adjunct to ultrasound in assessing NTD, as it pertains to pre-surgical planning and perinatal management. However, it should not be considered a replacement for ultrasonography, which continues to be the gold standard for fetal anatomic evaluation.
Topics: Disease Management; Humans; Magnetic Resonance Imaging; Meningomyelocele; Prenatal Diagnosis
PubMed: 28516216
DOI: 10.1007/s00381-017-3418-x -
Indian Journal of Pediatrics Dec 2002Terminal myelocystocele is an unusual form of occult spinal dysraphism. It consists of a cystic dilatation of a low-lying terminal cord herniated posteriorly through a...
Terminal myelocystocele is an unusual form of occult spinal dysraphism. It consists of a cystic dilatation of a low-lying terminal cord herniated posteriorly through a skin covered lumbosacral spina bifida. This condition is often associated with OEIS complex i.e. opmphalocele, exstrophy of the bladder, imperforate anus and spinal abnormality. We studied 4 cases of terminal myelocystocele. They revealed no preoperative neurological deficit. None of these had associated OEIS complex. One of the cyst was unique due to presence of copious amount of pus in its cavity. All four cases underwent successful repair and surgery remained uneventful in all of them. No child showed neurological deterioration during the follow-up.
Topics: Female; Humans; Infant, Newborn; Lumbosacral Region; Magnetic Resonance Imaging; Male; Meningomyelocele
PubMed: 12557964
DOI: 10.1007/BF02724394 -
No Shinkei Geka. Neurological Surgery Apr 1994
Review
Topics: Female; Fetal Diseases; Humans; Hydrocephalus; Infant, Newborn; Laminectomy; Meningomyelocele; Pregnancy; Ultrasonography, Prenatal
PubMed: 8164792
DOI: No ID Found -
Zhurnal Voprosy Neirokhirurgii Imeni N.... 1977Anterior sacral meningomyelocele is the rarest and least known form of congenital myelocele. It is not manifested externally, it is usually not attended with changes in...
Anterior sacral meningomyelocele is the rarest and least known form of congenital myelocele. It is not manifested externally, it is usually not attended with changes in the neurologic status, and may be regarded as a presacral dermoid cyst. The authors observed 5 members of one family with similar clinical and X-ray signs of such herniations, in 2 they were verified. The presence of cystic structures in the cavity of the small pelvis in conjunction with a congenital defect in the bodies of the sacral vertebrae is an indication for conducting pneumomyelography so as to make a more precise diagnosis. A study of the hereditary and family history is a necessary trend in the examination of such patients because the disease may be of a familial character.
Topics: Adult; Female; Humans; Male; Meningomyelocele; Middle Aged; Radiography; Sacrum
PubMed: 919974
DOI: No ID Found -
The Journal of the Oklahoma State... Jun 1977
Topics: Child, Preschool; Humans; Infant; Infant, Newborn; Intellectual Disability; Meningomyelocele; Patient Care Team; Prognosis; Spinal Dysraphism
PubMed: 328833
DOI: No ID Found