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Pediatric Cardiology 1984
Topics: Heart Block; Humans; Spleen
PubMed: 6531266
DOI: 10.1007/BF02427051 -
Asian Journal of Surgery Dec 2023
Topics: Humans; Heterotaxy Syndrome; Renal Veins; Tomography, X-Ray Computed
PubMed: 37541886
DOI: 10.1016/j.asjsur.2023.07.115 -
The Pan African Medical Journal 2022Polysplenia syndrome mainly described in pediatrics; rarely and incidentally in adulthood. Most patients had their diagnosis done during childhood due to the frequent...
Polysplenia syndrome mainly described in pediatrics; rarely and incidentally in adulthood. Most patients had their diagnosis done during childhood due to the frequent association to cardiac anomalies that speak for themselves earlier in life. Multiple spleens, cardiac defect and vascular malformation of the inferior vena cava with azygos or hemiazygos continuation are the most frequent observed malformations. Our patient was one this rarest adulthood incidental diagnosis, who presented in the emergency department for nephritic colic, and while imaging for this, multiples spleens and other visceral malformations were diagnosed. Hopefully, cardiac ultrasound hadn't showed any cardiac malformation and the patient was discharged aware of this condition. Through this publication we report the possible incidental diagnosis of polysplenia condition and highlight the fact that people with such important malformation can lead a normal life, and only awareness should be given for future surgeries, instrumental treatment or else.
Topics: Adult; Child; Echocardiography; Heterotaxy Syndrome; Humans; Vena Cava, Inferior
PubMed: 35371381
DOI: 10.11604/pamj.2022.41.67.29014 -
Journal of the Belgian Society of... 2022A rare case of spontaneous splenic infarction with polysplenia is presented. The diagnosis was made by confirmed by enhanced computed tomography (CT), which showed...
A rare case of spontaneous splenic infarction with polysplenia is presented. The diagnosis was made by confirmed by enhanced computed tomography (CT), which showed multiple spleens in the left abdomen and one of the spleen showing low attenuation areas representing infarct. Polysplenia syndrome is a rare entity associated with heterotaxy syndromes. Radiological examinations help the diagnosis by identifying infarcts in the spleen and other abnormal organs in the chest and abdomen. We report a rare case of polysplenic syndrome with splenic infarction.
PubMed: 35814278
DOI: 10.5334/jbsr.2685 -
Surgical and Radiologic Anatomy : SRA Oct 2013Polysplenia syndrome is classified as one of the situs ambiguous or heterotaxy syndromes and is classically termed left isomerism or bilateral left-sidedness. However,... (Review)
Review
Polysplenia syndrome is classified as one of the situs ambiguous or heterotaxy syndromes and is classically termed left isomerism or bilateral left-sidedness. However, polysplenia is a controversial and complex entity with no fixed pathognomonic features but rather a broad spectrum of abnormalities. In many published case series, polysplenia was neither associated with viscero-atrial heterotaxy nor with duplication of left-sided structures. The relationship between polysplenia and viscero-atrial situs is not clear. Several recent case reports describe the association of polysplenia with situs inversus totalis or with pancreatic; venous and other anomalies or with several types of malignancy. This article provides the reader with a review of the literature as well as our own experience aiming at better understanding of the polysplenia syndrome, its relationship with viscero-atrial situs and the spectrum of associated extra-cardiac anomalies.
Topics: Digestive System Abnormalities; Female; Heterotaxy Syndrome; Humans; Intestinal Volvulus; Middle Aged; Pancreas; Spleen; Tomography, X-Ray Computed
PubMed: 23508931
DOI: 10.1007/s00276-013-1100-x -
The Korean Journal of Internal Medicine Sep 2022
PubMed: 36131365
DOI: 10.3904/kjim.2022.209 -
The British Journal of Radiology Jun 1975Polysplenia is a rare syndrome of visceral anomalies. The diagnosis in vivo may be difficult. Recently Vaughan, Hawkins and Elliott (1971) stressed the importance of...
Polysplenia is a rare syndrome of visceral anomalies. The diagnosis in vivo may be difficult. Recently Vaughan, Hawkins and Elliott (1971) stressed the importance of visceral arteriography for a correct diagnosis. A patient with this condition was seen by us and the angiographic findings are reported hereby.
Topics: Adult; Aortography; Humans; Liver; Male; Spleen; Splenic Artery; Stomach
PubMed: 1227706
DOI: 10.1259/0007-1285-48-570-496 -
International Journal of Cardiology Jan 2019
Topics: Child; Child, Preschool; Follow-Up Studies; Heart Defects, Congenital; Heart Septal Defects, Ventricular; Heterotaxy Syndrome; Humans; Spleen
PubMed: 29980371
DOI: 10.1016/j.ijcard.2018.06.075 -
Journal of Visceral Surgery Oct 2011
Topics: Adult; Female; Heterotaxy Syndrome; Humans; Tomography, X-Ray Computed
PubMed: 22056515
DOI: 10.1016/j.jviscsurg.2011.09.013