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The Journal of Maternal-fetal &... Jul 2022The incidence of bilateral ductus arteriosus is sporadically reported in the uterus, and right aortic arch with aberrant of the left subclavian artery in association... (Review)
Review
Prenatal diagnosis of right aortic arch and aberrant left subclavian artery in association with bilateral ductus arteriosus by two-and four-dimensional echocardiography: a case of rare vascular ring and review of literature.
The incidence of bilateral ductus arteriosus is sporadically reported in the uterus, and right aortic arch with aberrant of the left subclavian artery in association with bilateral ductus arteriosus is therefore extremely rare. We describe a case of right aortic arch and aberrant left subclavian artery associated with bilateral ductus arteriosus. Scanning around the three-vessel and trachea view to search for an "O" shape and a "U" shape vascular ring is essential for the diagnosis, which reveals vascular structures coursing around the trachea. Four-dimensional echocardiography with high-definition flow imaging and spatiotemporal image correlation technique illustrates the spatial relationships of these vessels and the trachea, which should be considered as a complementary modality in fetal cardiac examinations.
Topics: Aorta, Thoracic; Cardiovascular Abnormalities; Ductus Arteriosus; Ductus Arteriosus, Patent; Echocardiography, Four-Dimensional; Female; Humans; Pregnancy; Prenatal Diagnosis; Subclavian Artery; Vascular Ring
PubMed: 32693651
DOI: 10.1080/14767058.2020.1795825 -
Ultraschall in Der Medizin (Stuttgart,... Dec 2022Congenital aortic vascular ring may present after birth with variable degrees of respiratory distress due to tracheal compression. The aim of this study was to...
OBJECTIVE
Congenital aortic vascular ring may present after birth with variable degrees of respiratory distress due to tracheal compression. The aim of this study was to prospectively evaluate in utero tracheal patency in correlation with postnatal outcome.
METHODS
During an eight-year period, fetuses with aortic arch abnormality encircling the trachea and forming a complete ring were recruited for the study. Tracheal patency was classified as: no compression, partial compression, or complete compression. Postnatal MRI/CTangio studies were performed and outcome data was retrospectively analyzed from the medical records.
RESULTS
Among the 46 fetuses recruited to the study, 38 had right aortic arch (RAA), and 8 presented with double aortic arch (DAA). In the RAA group 35 (92.1 %) of the fetuses presented no compression and 34 (97.1 %) of them were asymptomatic in the long-term follow-up. Three fetuses (7.9 %) in this group presented in utero compression: one was terminated at 16 weeks of gestation due to associated ominous findings, and the other two had mild respiratory symptoms around 12 months of age and underwent surgery with a good outcome. In the DAA group, all fetuses presented in utero with tracheal compression. Seven showed partial and one complete compression. Among the seven with partial compression, six were symptomatic and underwent surgery. The case with severe airway occlusion had emergency tube insertion in the delivery room and underwent surgery at 7 days but died from severe respiratory complications.
CONCLUSION
This is the first study to evaluate in utero tracheal patency in cases with vascular ring. It allows better prenatal and postnatal workup and follow-up including potentially life-threatening respiratory failure.
Topics: Pregnancy; Female; Humans; Vascular Ring; Trachea; Retrospective Studies; Aorta, Thoracic; Ultrasonography, Prenatal; Lung Diseases
PubMed: 33091939
DOI: 10.1055/a-1283-6051 -
Echocardiography (Mount Kisco, N.Y.) Dec 2020Vascular ring and sling are congenital anomalies of the vascular structure in the thorax with a prevalence of 2.4/10,000 live births. Double aortic arch (DAA), right...
Vascular ring and sling are congenital anomalies of the vascular structure in the thorax with a prevalence of 2.4/10,000 live births. Double aortic arch (DAA), right aortic arch with left ductus arteriosus and aberrant left subclavian artery (RAA-ALSA), and pulmonary artery sling (PAS) are the three common types of vascular ring and sling. These anomalies can be isolated or accompanied by intracardiac malformation. The presence of both vascular ring and PAS is extremely rare. Here, we report a fetus who was prenatally diagnosed with PAS and RAA-ALS, and developed symptoms due to esophageal and airway compression after birth.
Topics: Aorta, Thoracic; Ductus Arteriosus; Humans; Retrospective Studies; Vascular Ring
PubMed: 33107081
DOI: 10.1111/echo.14907 -
Pediatrics International : Official... Feb 2017Vascular rings may cause pressure on the trachea and/or esophagus of varying degree, resulting in symptoms. This study assessed the presentation symptoms, diagnostic...
BACKGROUND
Vascular rings may cause pressure on the trachea and/or esophagus of varying degree, resulting in symptoms. This study assessed the presentation symptoms, diagnostic methods and treatment results after surgery in children with vascular ring.
METHODS
Symptomatic vascular ring patients undergoing surgery between January 2010 and August 2014 at Mehmet Akif Ersoy Cardiovascular Research and Training Hospital, Istanbul, were retrospectively assessed. The presentation symptoms, demographic characteristics, and diagnostic tests were evaluated. Operative data and postoperative follow up, complications and problems were also examined in detail.
RESULTS
Twenty-one patients underwent surgery, 13 (63%) of whom were male. Median age was 12 months (range, 1 month-8 years). Among these patients, 62% (n = 13) had double aortic arch, 24% (n = 5) had right-sided aortic arch + ligamentum arteriosum, 10% (n = 2) had left-sided aortic arch + aberrant right subclavian artery, and 4% (n = 1) had pulmonary sling abnormality. Computed tomography (CT) angiography was performed in 17/21 patients. All the patients were successfully operated on. In the early postoperative period, two patients had chylothorax and one had nerve paralysis of nervus laryngeus recurrens. One patient died in the early period, and two patients had ongoing stridor on follow up.
CONCLUSIONS
CT angiography is effective for the differential diagnosis and visualization of vascular ring abnormality. In such cases, full recovery can be assured with early diagnosis and surgery.
Topics: Aorta, Thoracic; Child; Child, Preschool; Computed Tomography Angiography; Diagnosis, Differential; Esophageal Stenosis; Female; Follow-Up Studies; Humans; Infant; Male; Postoperative Complications; Retrospective Studies; Tracheal Stenosis; Treatment Outcome; Vascular Malformations
PubMed: 27454661
DOI: 10.1111/ped.13101 -
Clinical Imaging 2015Button battery ingestion can lead to dangerous complications, including vasculoesophageal fistula formation. The presence of a vascular ring may complicate battery...
Button battery ingestion can lead to dangerous complications, including vasculoesophageal fistula formation. The presence of a vascular ring may complicate battery ingestion if the battery lodges at the level of the ring and its important vascular structures. We report a 4-year-old boy with trisomy 21 who was diagnosed with a vascular ring at the time of button battery ingestion and died 9 days after presentation due to massive upper gastrointestinal bleeding from esophageal erosion and vasculoesophageal fistula formation.
Topics: Child, Preschool; Electric Power Supplies; Esophageal Diseases; Esophageal Fistula; Esophagus; Fatal Outcome; Foreign Bodies; Gastrointestinal Hemorrhage; Humans; Male; Ulcer
PubMed: 25662210
DOI: 10.1016/j.clinimag.2015.01.009 -
Radiology Case Reports Dec 2022We present a case of a vascular ring formed by the left brachiocephalic vein. A left brachiocephalic vein ring or circum-aortic left brachiocephalic vein is a rare...
We present a case of a vascular ring formed by the left brachiocephalic vein. A left brachiocephalic vein ring or circum-aortic left brachiocephalic vein is a rare congenital vascular variant. Although it is usually an incidental finding on chest imaging studies, left brachiocephalic vein anomalies, particularly the ring variant, can be clinically significant during procedures requiring installation of transvenous implantable devices such as pacemakers. In this report, we illustrate the appearance on computed tomography of this rare anomaly and discuss an embryological hypothesis for the etiology.
PubMed: 36281284
DOI: 10.1016/j.radcr.2022.09.077 -
The Annals of Thoracic Surgery Jan 2022
Topics: Aorta, Thoracic; Brachiocephalic Veins; Esophagus; Humans; Infant; Male; Vascular Ring
PubMed: 34560042
DOI: 10.1016/j.athoracsur.2021.08.027 -
Journal of the Saudi Heart Association Jan 2018Kommerell's diverticulum is a rare saccular aneurysmal dilation of the descending aorta. We report a case of a 3.5-year-old boy with the extremely rare combination of...
Kommerell's diverticulum is a rare saccular aneurysmal dilation of the descending aorta. We report a case of a 3.5-year-old boy with the extremely rare combination of Kommerell's diverticulum with a right descending aorta and proximal patent ductus arteriosus aneurysm forming an incomplete vascular ring. To our knowledge, this rare case has not been reported to date.
PubMed: 29296067
DOI: 10.1016/j.jsha.2017.04.005 -
Translational Pediatrics Apr 2017
PubMed: 28503412
DOI: 10.21037/tp.2017.03.05