Disease or Syndrome
Scimitar syndrome
Scim·i·tar syn·drome
Subclass of:
Congenital abnormality of respiratory system; Vascular Diseases; Vascular anomaly; Lung diseases
Definitions related to scimitar syndrome:
  • (scimitar anomaly) Right pulmonary venous return to the inferior vena cava.
    Human Phenotype Ontology (HPO)
    The Human Phenotype Ontology Project, 2025
  • A rare congenital cardiopulmonary defect characterized by abnormal right-sided pulmonary venous drainage and right lung malformations.
    NCI
    U.S. National Cancer Institute, 2021
  • An anomalous pulmonary venous return in which the right PULMONARY VEIN is not connected to the LEFT ATRIUM but to the INFERIOR VENA CAVA. Scimitar syndrome is named for the crescent- or Turkish sword-like shadow in the chest radiography and is often associated with hypoplasia of the right lung and right pulmonary artery, and dextroposition of the heart.
    NLM Medical Subject Headings
    U.S. National Library of Medicine, 2025
  • A rare developmental defect during embryogenesis where some or all of the pulmonary veins drain into the right atrium or the systemic veins, with or without the presence of pulmonary venous obstruction, leading to various manifestations such as fatigue, exertional dyspnea, pulmonary arterial hypertension, cyanosis and progressive...
    NIH Genetic and Rare Diseases
    National Center for Advancing Translational Sciences
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