Disease or Syndrome
job syndrome
job syn·drome
Subclass of:
Primary immune deficiency disorder;
Phagocyte Bactericidal Dysfunction
Also called:
Hyper-IgE Syndrome; Buckley Syndrome; Hyperimmunoglobulinemia E Syndrome
Definitions related to job syndrome:
-
Primary immunodeficiency syndrome characterized by recurrent infections and hyperimmunoglobulinemia E. Most cases are sporadic. Of the rare familial forms, the dominantly inherited subtype has additional connective tissue, dental and skeletal involvement that the recessive type does not share.NLM Medical Subject HeadingsU.S. National Library of Medicine, 2021
-
(hyperimmunoglobulin e syndrome) A condition that is characterized by elevated serum IgE, dermatitis, and respiratory infections.NCI ThesaurusU.S. National Cancer Institute, 2021
-
Hyper-IgE syndrome is a hereditary combined B- and T-cell immunodeficiency characterized by recurrent staphylococcal abscesses of the skin, sinopulmonary infections, and severe pruritic eosinophilic dermatitis. Diagnosis is confirmed by measurement of serum IgE levels. Treatment consists of supportive measures, including lifelong...Merck & Co., Inc., 2020
-
Autosomal dominant hyperimmunoglobulin E (IgE) syndrome (HIES) was first described as Job syndrome in 1966 and included the triad of eosinophilia, eczema, and recurrent skin and pulmonary infections (named after the biblical character Job, who wasWebMD, 2019
-
Hyper IgE syndromes (HIES) are rare primary immune deficiencies characterized by elevated serum IgE, skin inflammation (dermatitis) and recurrent skin and lung infections. There are two forms of HIES, which have the above characteristics in common but otherwise have distinct presentations, courses and outcomes: autosomal dominant HIES...National Center for Advancing Translational Sciences
Return to OpenMD Medical Dictionary
> J
This content should not be used in place of medically-reviewed decision support reference material or professional medical advice. Some terms may have alternate or updated definitions not reflected in this set. The definitions on this page should not be considered complete or up to date.