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Journal of Cardiac Surgery Apr 2022A staged thoracotomy unifocalization approach has not been the dominant option over the past 20 years primarily due to the introduction of midline one-stage complete...
BACKGROUND
A staged thoracotomy unifocalization approach has not been the dominant option over the past 20 years primarily due to the introduction of midline one-stage complete unifocalization.
METHODS
In this issue of the Journal of Cardiac Surgery, van de Woestijne et al. publish their experience over the past 30 years in 39 consecutive patients with "consistent" staged unifocalization through a lateral thoracotomy in patients with pulmonary atresia, ventricular septal defect, and major aortopulmonary collateral arteries (PA/VSD/MAPCA).
RESULTS
They report definitive repair completion in 76.3% of the patients and an overall survival after definitive repair of 96% at 20 years despite the study period ranging from 1989 to the present.
CONCLUSION
Given the multiple variations one could have with PA/VSD/MPACA, a midline unifocalization approach may not always be possible. Surgeons should be familiar with the lateral thoracotomy unifocalization staged approach to PA/VSD/MAPCA.
Topics: Cardiac Surgical Procedures; Collateral Circulation; Heart Septal Defects, Ventricular; Humans; Infant; Pulmonary Artery; Pulmonary Atresia; Retrospective Studies
PubMed: 35137983
DOI: 10.1111/jocs.16296 -
The Journal of Thoracic and... Jan 2022
Topics: Adult; Cardiovascular Surgical Procedures; Female; Humans; Infant; Long Term Adverse Effects; Male; Postoperative Complications; Reoperation; Risk Assessment; Risk Factors; Survival Analysis; Truncus Arteriosus, Persistent
PubMed: 33726910
DOI: 10.1016/j.jtcvs.2021.01.137 -
European Journal of Cardio-thoracic... Nov 2022
Topics: Humans; Pulmonary Atresia; Tetralogy of Fallot; Pulmonary Artery; Heart Defects, Congenital
PubMed: 36321990
DOI: 10.1093/ejcts/ezac523 -
Indian Journal of Thoracic and... Sep 2021Berry syndrome is a rare congenital cardiac anomaly, characterized by distal aortopulmonary window, hypoplasia or interruption of the aortic arch, intact ventricular... (Review)
Review
Berry syndrome is a rare congenital cardiac anomaly, characterized by distal aortopulmonary window, hypoplasia or interruption of the aortic arch, intact ventricular septum, and aortic origin of the right pulmonary artery and patent ductus arteriosus. Anatomic depiction of each component is important for the diagnosis. Single-stage surgical repair is challenging but feasible with good survival outcomes. The available literature on this anomaly is limited. Hence, this paper aims at reviewing the literature on Berry syndrome.
PubMed: 34511759
DOI: 10.1007/s12055-021-01206-0 -
Journal of Cardiac Surgery Sep 2022Pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries (PA/VSD/MAPCA) represents an anatomically diverse and technically demanding... (Review)
Review
Pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries (PA/VSD/MAPCA) represents an anatomically diverse and technically demanding spectrum of congenital disease. Here, we review a manuscript by Onalan et al. in the Journal of Cardiac Surgery detailing a retrospective, single-center cohort study of patients undergoing unifocalization for PA/VSD/MAPCA via either a pulmonary artery patch augmentation or pericardial roll technique. While they report statistically equivalent outcomes using both techniques, longer follow-up and increased sample size are necessary to determine efficacy and safety.
Topics: Cohort Studies; Collateral Circulation; Heart Septal Defects, Ventricular; Humans; Infant; Pulmonary Artery; Pulmonary Atresia; Retrospective Studies
PubMed: 35661266
DOI: 10.1111/jocs.16651 -
Multimedia Manual of Cardiothoracic... Dec 2020Truncus arteriosus, an anomaly of the conotruncus, is an extremely rare congenital heart disease that affects 1.19% of all patients with congenital heart diseases. We...
Truncus arteriosus, an anomaly of the conotruncus, is an extremely rare congenital heart disease that affects 1.19% of all patients with congenital heart diseases. We present a surgical technique using an 8-mm cryopreserved aortic root homograft in the aortic position and a 12-mm pulmonary valved conduit in the right position that allowed us to correct this rare congenital malformation. The cryopreserved aortic root homograft was considered a priority option for surgical correction. The neonatal Bentall (micro-Bentall) procedure is a surgically demanding procedure but can be performed successfully by an experienced surgeon. If we were performing a non-salvage procedure, we would have chosen a decellularized allograft.
Topics: Aorta, Thoracic; Cardiac Surgical Procedures; Cryopreservation; Echocardiography; Humans; Infant, Newborn; Transplantation, Homologous; Truncus Arteriosus, Persistent
PubMed: 33577148
DOI: 10.1510/mmcts.2020.079