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The Journal of Thoracic and... Jan 2022
Topics: Adult; Cardiovascular Surgical Procedures; Female; Humans; Infant; Long Term Adverse Effects; Male; Postoperative Complications; Reoperation; Risk Assessment; Risk Factors; Survival Analysis; Truncus Arteriosus, Persistent
PubMed: 33726910
DOI: 10.1016/j.jtcvs.2021.01.137 -
Journal of Cardiac Surgery Sep 2022Pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries (PA/VSD/MAPCA) represents an anatomically diverse and technically demanding... (Review)
Review
Pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries (PA/VSD/MAPCA) represents an anatomically diverse and technically demanding spectrum of congenital disease. Here, we review a manuscript by Onalan et al. in the Journal of Cardiac Surgery detailing a retrospective, single-center cohort study of patients undergoing unifocalization for PA/VSD/MAPCA via either a pulmonary artery patch augmentation or pericardial roll technique. While they report statistically equivalent outcomes using both techniques, longer follow-up and increased sample size are necessary to determine efficacy and safety.
Topics: Cohort Studies; Collateral Circulation; Heart Septal Defects, Ventricular; Humans; Infant; Pulmonary Artery; Pulmonary Atresia; Retrospective Studies
PubMed: 35661266
DOI: 10.1111/jocs.16651 -
Indian Journal of Thoracic and... Sep 2021Berry syndrome is a rare congenital cardiac anomaly, characterized by distal aortopulmonary window, hypoplasia or interruption of the aortic arch, intact ventricular... (Review)
Review
Berry syndrome is a rare congenital cardiac anomaly, characterized by distal aortopulmonary window, hypoplasia or interruption of the aortic arch, intact ventricular septum, and aortic origin of the right pulmonary artery and patent ductus arteriosus. Anatomic depiction of each component is important for the diagnosis. Single-stage surgical repair is challenging but feasible with good survival outcomes. The available literature on this anomaly is limited. Hence, this paper aims at reviewing the literature on Berry syndrome.
PubMed: 34511759
DOI: 10.1007/s12055-021-01206-0 -
Multimedia Manual of Cardiothoracic... Dec 2020Truncus arteriosus, an anomaly of the conotruncus, is an extremely rare congenital heart disease that affects 1.19% of all patients with congenital heart diseases. We...
Truncus arteriosus, an anomaly of the conotruncus, is an extremely rare congenital heart disease that affects 1.19% of all patients with congenital heart diseases. We present a surgical technique using an 8-mm cryopreserved aortic root homograft in the aortic position and a 12-mm pulmonary valved conduit in the right position that allowed us to correct this rare congenital malformation. The cryopreserved aortic root homograft was considered a priority option for surgical correction. The neonatal Bentall (micro-Bentall) procedure is a surgically demanding procedure but can be performed successfully by an experienced surgeon. If we were performing a non-salvage procedure, we would have chosen a decellularized allograft.
Topics: Aorta, Thoracic; Cardiac Surgical Procedures; Cryopreservation; Echocardiography; Humans; Infant, Newborn; Transplantation, Homologous; Truncus Arteriosus, Persistent
PubMed: 33577148
DOI: 10.1510/mmcts.2020.079 -
World Journal For Pediatric &... May 2022
PubMed: 35446207
DOI: 10.1177/21501351221083987 -
Radiology. Cardiothoracic Imaging Jun 2022Conotruncal anomalies, also referred to as outflow tract anomalies, are congenital heart defects that result from abnormal septation of the great vessels' outflow... (Review)
Review
Conotruncal anomalies, also referred to as outflow tract anomalies, are congenital heart defects that result from abnormal septation of the great vessels' outflow tracts. The major conotruncal anomalies include tetralogy of Fallot, double-outlet right ventricle, transposition of the great arteries, truncus arteriosus, and interrupted aortic arch. Other defects, which are often components of the major anomalies, include pulmonary atresia with ventricular septal defect, pulmonary valve agenesis, aortopulmonary window, and double-outlet left ventricle. CT has emerged as a robust diagnostic tool in preoperative and postoperative assessment of various congenital heart diseases, including conotruncal anomalies. The data provided with multidetector CT imaging are useful for treatment planning and follow-up monitoring after surgery or intervention. Unlike echocardiography and MRI, CT is not limited by a small acoustic window, metallic devices, and need for sedation or anesthesia. Major advances in CT equipment, including dual-source scanners, wide-detector scanners, high-efficiency detectors, higher x-ray tube power, automatic tube current modulation, and advanced three-dimensional postprocessing, provide a low-risk, high-quality alternative to diagnostic cardiac catheterization and MRI. This review explores the various conotruncal anomalies and elucidates the role of CT imaging in their pre- and postoperative assessment. CT, CT Angiography, Stents, Pediatrics © RSNA, 2022.
PubMed: 35923747
DOI: 10.1148/ryct.210089