-
Hong Kong Medical Journal = Xianggang... Dec 2020
Topics: Diagnosis, Differential; Female; Humans; Kidney Calices; Kidney Diseases; Medical Illustration; Radiography; Young Adult
PubMed: 33350970
DOI: 10.12809/hkmj208463 -
Urology May 1982Megacalycosis is a primary disease of the renal calyx which is diagnosed usually because of its complications, such as calculi or infections in the urinary tract. In the...
Megacalycosis is a primary disease of the renal calyx which is diagnosed usually because of its complications, such as calculi or infections in the urinary tract. In the absence of complications, the disease is discovered accidentally in the course of urologic examination undertaken for a different reason. The present article reports 4 cases of megacalycosis: one with histologic confirmation in addition to radiologic diagnostic criteria and 3 with diagnosis based on radiologic findings alone. Alertness to the possible existence of megacalycosis in patients suffering from infections and calculi in the urinary tract contributes to and facilitates choice of appropriate treatment.
Topics: Dilatation, Pathologic; Humans; Hydronephrosis; Kidney Calices; Kidney Medulla; Kidney Pelvis; Male; Middle Aged; Prognosis; Urinary Calculi; Urinary Tract Infections; Urography
PubMed: 7080319
DOI: 10.1016/0090-4295(82)90602-1 -
European Journal of Pediatric Surgery :... Feb 1996The authors report a rare case of megacalycosis located on a duplex system upper moiety, and analyse the problems related to its pathology, etiopathogenesis, clinical... (Review)
Review
The authors report a rare case of megacalycosis located on a duplex system upper moiety, and analyse the problems related to its pathology, etiopathogenesis, clinical manifestations and diagnosis.
Topics: Dilatation, Pathologic; Female; Humans; Infant; Kidney Calices; Radiography; Radionuclide Imaging; Technetium Tc 99m Pentetate; Ultrasonography, Doppler, Duplex; Ureter
PubMed: 8721180
DOI: 10.1055/s-2008-1066468 -
Clinical Case Reports Feb 2021Recurrent UTI's represent a challenge for physicians and anatomic abnormalities should be investigated thoroughly in this setting. Not all urinary tract dilatations mean...
Recurrent UTI's represent a challenge for physicians and anatomic abnormalities should be investigated thoroughly in this setting. Not all urinary tract dilatations mean obstruction. Several entities can mimic hydronephrosis without actual interruption of urinary flow. Uniform calyceal dilatation without dilatation of pelvis and ureter suggests megacalycosis.
PubMed: 33598298
DOI: 10.1002/ccr3.3687 -
Archivos Espanoles de Urologia Apr 1995Megacalycosis or Puigvert's disease is a clinical entity characterized by dilatation of all renal calyces without dilatation of the renal pelvis or ureter in the absence... (Review)
Review
OBJECTIVES
Megacalycosis or Puigvert's disease is a clinical entity characterized by dilatation of all renal calyces without dilatation of the renal pelvis or ureter in the absence of any obstructive factor. To date, its pathogenesis remains unclear. The rarity of this disease and the importance of making a correct differential diagnosis prompted us to report on the present case.
METHODS/RESULTS
Two patients with urolithiasis associated with ipsilateral megacalyces who were successfully treated by ESWL are described. The clinical, diagnostic and therapeutic aspects reported in the literature are briefly reviewed.
CONCLUSIONS
There is a greater lithogenic predisposition in these patients. Intravenous urography has proved to be very accurate in making the differential diagnosis from other disorders such as obstructive uropathy and intermittent hydronephrosis. The efficacy of ESWL in the treatment of lithiasis associated with megacalycosis is underscored. A yearly control follow up by analyses and intravenous urography is advocated.
Topics: Chronic Disease; Dilatation, Pathologic; Emergencies; Humans; Kidney Calculi; Kidney Calices; Lithotripsy; Male; Middle Aged; Radiography; Syndrome; Ultrasonography
PubMed: 7755440
DOI: No ID Found -
Ryoikibetsu Shokogun Shirizu 1997
-
Current Opinion in Urology Jul 2023Nowadays, due to the increase of imaging diagnosis, we identify easily renal anomalies, and we can choose between a wide range of armamentarium to treat symptomatic... (Review)
Review
Retrograde intrarenal surgery for stones associated with renal anomalies: caliceal diverticulum, horseshoe kidney, medullary sponge kidney, megacalycosis, pelvic kidney, uretero-pelvic junction obstruction.
PURPOSE OF REVIEW
Nowadays, due to the increase of imaging diagnosis, we identify easily renal anomalies, and we can choose between a wide range of armamentarium to treat symptomatic stones in those challenging cases. However, there is a lack of evidence and consensus on its use. The aim of this narrative review is to collect all the available data about safety and efficacity of retrograde intrarenal surgery (RIRS) in the treatment of kidney stones associated to a renal anomaly.
RECENT FINDINGS
Renal anomalies are uncommon findings and even more if it has to be associated with renal stones. After a literature review of the past 2 years, there are a small number of studies that compare the outcomes in patients who have been treated with minimally invasive modalities and they are mainly focus on RIRS.
SUMMARY
It is of extreme importance to know the advances on the stone treatment in anomalous kidneys. With the development of new laser technologies, RIRS is becoming a more interesting technique with high success rate and safety. Further studies are needed to make an accurate statement about the adequate surgical technique for each renal anomaly and also, clinical trials using new laser technologies.
Topics: Humans; Fused Kidney; Medullary Sponge Kidney; Treatment Outcome; Kidney Calculi; Kidney; Diverticulum; Retrospective Studies; Nephrostomy, Percutaneous
PubMed: 37014757
DOI: 10.1097/MOU.0000000000001093 -
Pediatric Nephrology (Berlin, Germany) May 2009Megacalycosis is an extremely rare condition. We report our experience with two cases and discuss its pathogenesis, diagnosis and management in children. Our two...
Megacalycosis is an extremely rare condition. We report our experience with two cases and discuss its pathogenesis, diagnosis and management in children. Our two patients had presented a prior diagnosis of congenital hydronephrosis. An increased number of calyces with a significant disproportion between the degree of calyceal dilatation and a mildly dilated renal pelvis were found in each case. Megacalycosis must be considered in the differential diagnosis of congenital hydronephrosis, polycalycosis, and infundibular stenosis. The diagnosis is suggested by ultrasound and confirmed by diuretic renography, intravenous pyelography or magnetic resonance urography. Voiding cystourethrography should be performed to rule out vesicoureteral reflux. A high index of suspicion is needed for the diagnosis of this condition.
Topics: Child, Preschool; Diagnosis, Differential; Dilatation, Pathologic; Female; Humans; Hydronephrosis; Infant; Kidney Calices; Magnetic Resonance Imaging; Male; Ultrasonography; Urography
PubMed: 19002724
DOI: 10.1007/s00467-008-1039-z -
Radiographics : a Review Publication of... 2021The upper urinary tract is the most common human system affected by congenital anomalies. Congenital anomalies of the kidneys and ureters comprise a wide spectrum of... (Review)
Review
The upper urinary tract is the most common human system affected by congenital anomalies. Congenital anomalies of the kidneys and ureters comprise a wide spectrum of disorders ranging from simple variants with no clinical significance to complex anomalies that may lead to severe complications and end-stage renal disease. They may be classified as anomalies of renal form, which are subclassified as structural anomalies (eg, persistent fetal lobulation, hypertrophied column of Bertin, and dromedary hump) and fusion anomalies (eg, horseshoe kidney and pancake kidney); anomalies of renal position (eg, renal malrotation, simple renal ectopia, and crossed renal ectopia) and renal number (eg, renal agenesis and supernumerary kidney); and abnormalities in development of the urinary collecting system (eg, pyelocaliceal diverticulum, megacalycosis, ureteropelvic junction obstruction, duplex collecting system, megaureter, ectopic ureter, and ureterocele). US is usually the first imaging modality used because of its low cost, wide availability, and absence of ionizing radiation. Intravenous urography and voiding cystourethrography are also useful, mainly for characterization of the collecting system and vesicoureteral reflux. However, intravenous urography has been replaced by CT urography and MR urography. These imaging methods not only allow direct visualization of the collecting system but also demonstrate the function of the kidneys, the vascular anatomy, adjacent structures, and complications. Comprehension of congenital anomalies of the upper urinary tract is crucial for an accurate diagnosis and correct management. The authors discuss the spectrum of these anomalies, with emphasis on embryologic development, imaging findings, clinical manifestations, and complications. RSNA, 2021.
Topics: Humans; Kidney; Ureter; Urinary Tract; Urogenital Abnormalities; Urography
PubMed: 33513074
DOI: 10.1148/rg.2021200078 -
IJU Case Reports Jul 2023Megacalycosis is a rare disorder related to congenital underdevelopment of the renal papilla or structural defect of the renal calyces. Megacalycosis has a wide spectrum...
INTRODUCTION
Megacalycosis is a rare disorder related to congenital underdevelopment of the renal papilla or structural defect of the renal calyces. Megacalycosis has a wide spectrum of clinical presentations ranging from simple variants without any significance on renal function to severe complications. Any prevention strategy is recommended yet since megacalycosis is mostly asymptomatic and usually discovered either accidentally or as result of its complications.
CASE PRESENTATION
We observed megacalycosis progression in a young female with a single kidney toward progressive calyx dilatation for years, which ended in acute pyelonephritis. Conservative management, urinary drainage, and large-spectrum antibiotics were unsuccessful and nephrectomy was required.
CONCLUSION
This rare case and literature review add evidence to identify prognostic factors to select patients with a high risk of complications (single kidney, bilateral disease, female gender, associated genetic syndromes, vesicoureteral reflux, and contralateral renal disorder). One o more factors should activate close monitoring and prophylactic therapy if needed.
PubMed: 37405038
DOI: 10.1002/iju5.12597